CONGENITAL HEART DISEASE FULL BOOK
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Cyanotic heart diseases
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Heterotaxy Syndrome
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Dextrocardia
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Aortopulmonary Window
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AVSD
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PDA
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ABSENT PULMONARY VALVE SYNDROME
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ADULTS WITH CYANOTIC CONGENITAL HEART DISEASES
Adults with Cyanotic Congenital Heart Diseases
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ANOMALOUS LEFT CORONARY ARTERY FROM THE PULMONARY ARTERY (ALCAPA)
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ANEURYSM OF THE SINUS OF VALSALVA
ANEURYSM OF THE SINUS OF VALSALVA
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AORTIC ARCH DEVELOPMENT
AORTIC ARCH DEVELOPMENT
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APPROACHES TO CYANOTIC HEART DISEASE
APPROACHES TO CYANOTIC HEART DISEASE
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AORTOPULMONARY WINDOW (APW)
APW
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ANOMALOUS RIGHT CORONARY ARTERY FROM THE PULMONARY ARTERY (ARCAPA)
ANOMALOUS RIGHT CORONARY ARTERY FROM THE PULMONARY ARTERY (ARCAPA)
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ATRIOVENTRICULAR SEPTAL DEFECT (AVSD)
Atrioventricular septal defect (AVSD), also known as atrioventricular canal defect or endocardial cushion defect,
is a complex congenital heart defect involving a malformation of the atrioventricular (AV) septum, AV valves,
and the endocardial cushions. This condition disrupts the normal formation of the septum between the atria
and ventricles, as well as the development of the mitral and tricuspid valves. AVSD is commonly associated with
genetic conditions, particularly Down syndrome (Trisomy 21), and is classified into different types based on the
extent and location of the defect.
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BEDSIDE DIAGNOSIS OF ACYANOTIC CONGENITAL HEART DISEASES (CHDS)
Acyanotic congenital heart diseases (CHDs) refer to congenital heart defects that do not typically
cause cyanosis (a bluish discoloration of the skin due to low oxygen levels) under normal conditions.
In these conditions, the blood flow is usually shunted from left to right, meaning oxygenated blood
from the left side of the heart flows back to the right side, resulting in increased pulmonary blood
flow but no mixing of deoxygenated blood into systemic circulation. This keeps oxygen saturation
close to normal, hence "acyanotic."
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BICUSPID AORTIC VALVE
A bicuspid aortic valve (BAV) is a congenital heart defect where the aortic valve has two leaflets (cusps) instead
of the usual three. This anomaly results in abnormal valve structure, which can lead to aortic valve dysfunction,
particularly aortic stenosis (AS) or aortic regurgitation (AR), over time. BAV is one of the most common
congenital heart anomalies, occurring in approximately 1-2% of the population.
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CARE OF THE ADULT WITH CYANOTIC CONGENITAL HEART DISEASE
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CLASSIFICATION OF CARDIOVASCULAR ANOMALIES BASED ON SITUS
"Situs" refers to the orientation and arrangement of organs within the body, particularly in relation
to the left-right axis. In cardiovascular anomalies, "situs" classification is crucial for understanding
the spatial organization of the heart and associated structures. The classification is based on the
arrangement of the heart, major vessels, and organs (such as the liver, stomach, and spleen). Here is
an overview of the different situs classifications and related terminologies used in cardiovascular
anomalies.
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COARCTATION OF THE AORTA
COARCTATION OF THE AORTA
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COMMON ATRIUM
COMMON ATRIUM
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CONGENITAL HEART BLOCKS AND BRADYARRHYTHMIAS
CONGENITAL HEART BLOCKS AND BRADYARRHYTHMIAS
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CONGENITAL PULMONARY ARTERIOVENOUS FISTULA
CONGENITAL PULMONARY ARTERIOVENOUS FISTULA
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COR TRIATRIATUM
COR TRIATRIATUM
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CORONARY ARTERIES ANAOMLIES
CORONARY ARTERIES ANAOMLIES
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CORONARY ARTERY FISTULA
CORONARY ARTERY FISTULA
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DILATED CARDIOMYOPATHY
DILATED CARDIOMYOPATHY
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DOUBLE OUTLET RIGHT VENTRICLE (DORV)
DOUBLE OUTLET RIGHT VENTRICLE (DORV)
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DUCT DEPENDENT PULMONARY CIRCULATION
DUCT DEPENDENT PULMONARY CIRCULATION
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DUCT DEPENDENT SYSTEMIC CIRCULATION
DUCT DEPENDENT SYSTEMIC CIRCULATION
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EBSTEIN ANOMALY
EBSTEIN ANOMALY
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ECTOPIA CORDIS
ECTOPIA CORDIS
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EMBRYOLOGY OF HEART
EMBRYOLOGY OF HEART
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EMBRYOLOGY OF THE INFERIOR VENA CAVA
EMBRYOLOGY OF THE INFERIOR VENA CAVA
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EMBRYOLOGY OF THE PULMONARY VEINS
EMBRYOLOGY OF THE PULMONARY VEINS
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EMBRYOLOGY OF THE SUPERIOR VENA CAVA (SVC) AND ITS ANOMALIES
EMBRYOLOGY OF THE SUPERIOR VENA CAVA (SVC) AND ITS ANOMALIES EDITED
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ENDOCARDIAL FIBROELASTOSIS
ENDOCARDIAL FIBROELASTOSIS
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FETAL CIRCULATION
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FETZL ECHO
FETZL ECHO
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FONTAN CIRCULATION
FONTAN CIRCULATION
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GENETIC DISORDERS ASSOCIATED WITH CONGENITAL HEART DISEASE
GENETIC DISORDERS ASSOCIATED WITH CONGENITAL HEART DISEASE
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HEROTOXY
HEROTOXY
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HYPERVISCOSITY SYNDROME
HYPERVISCOSITY SYNDROME
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HYPOPLASTIC LEFT HEART SYNDROME
HYPOPLASTIC LEFT HEART SYNDROME
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INTERRUPTION OF THE AORTIC ARCH
INTERRUPTION OF THE AORTIC ARCH
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MATERNAL DRUGS & HEART DISEASES.
MATERNAL DRUGS & HEART DISEASES.
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MATERNAL INFECTIONS & HEART DISEASES.
MATERNAL INFECTIONS & HEART DISEASES.
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MITRAL VALVE PROLAPSE
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MORPHOLOGICAL FEATURES OF VARIOUS CARDIAC CHAMBERS AND GREAT ARTERIES
MORPHOLOGICAL FEATURES OF VARIOUS CARDIAC CHAMBERS AND GREAT ARTERIES
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NON COMPACTION OF VENTRICLES
NON COMPACTION OF VENTRICLES
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PALLIATIVE PROCEDURES IN CONGENITAL HEART DISEASE
PALLIATIVE PROCEDURES IN CONGENITAL HEART DISEASE
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OBSTRUCTIONS AT THE MITRAL VALVE
OBSTRUCTIONS AT THE MITRAL VALVE
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PATENT DUCTUS ARTERIOSUS
PATENT DUCTUS ARTERIOSUS
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PATERNAL MEDICAL CONDITION & HEART DISEASE
PATERNAL MEDICAL CONDITION & HEART DISEASE
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PERSISTENT LEFT SUPERIOR VENA CAVA EDITED
PERSISTENT LEFT SUPERIOR VENA CAVA EDITED
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PRECONCEPTION ASSESSMENT FOR PREGNANCY RISK ASSESSMENT IN WOMEN WITH CONGENITA L HEART DISEASES
PRECONCEPTION ASSESSMENT FOR PREGNANCY RISK ASSESSMENT IN WOMEN WITH CONGENITA L HEART DISEASES
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PULMONARY ARTERY STENOSIS
PULMONARY ARTERY STENOSIS
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PULSEOXY
PULSEOXY
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RESTRICTIVE CARDIOMYOPATHY
RESTRICTIVE CARDIOMYOPATHY
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SCIMITAR SYNDROME
SCIMITAR SYNDROME
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SHONE
SHONE
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SINGLE VENTRICLE
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SUBAORTIC STENOSIS
SUBAORTIC STENOSIS
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SUPRAVALVULAR AORTIC STENOSIS
SUPRAVALVULAR AORTIC STENOSIS
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TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION
TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION
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TRICUSPID ATRESIA
TRICUSPID ATRESIA
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VALVAR AORTIC STENOSIS
VALVAR AORTIC STENOSIS
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VALVAR PULMONARY STENOSIS
VALVAR PULMONARY STENOSIS
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VASCULAR SLINGS AND RINGS
VASCULAR SLINGS AND RINGS
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VENTRICULOARTERIAL JUNCTION
VENTRICULOARTERIAL JUNCTION
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